Giant Askin tumor: a diagnosis and therapeutic challenge.

نویسندگان

  • R Younus
  • A Khan
  • S Syed
چکیده

In 1979, Askin and colleagues suggested a distinct clin icopathological entity, characterized by small round blue cell tumor ofthoracopulmonary region (Askin tumor), with varying degrees of neuronal differentiation 1 . Various designations have been used to describe this tumor, such as: adult neurob lastom a, peripheral neuroblastoma, peripheral neuroepithel iom a, primitive n euroectodermal tumor and Ewing’ s sarcoma family of tumors. Askin tumor is seen in children and adolescents with a 3:I female predominance. It is a highly malignant tumor with a very poor prognosis 2 . For advances to be made in treating these patients, therapy should be given in a multidisciplinary manner in the context of’ a clinical trial at a major medical centre that has expertise in managing such patients.

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عنوان ژورنال:
  • JPMA. The Journal of the Pakistan Medical Association

دوره 52 2  شماره 

صفحات  -

تاریخ انتشار 2002